ea0032p557 | Endocrine tumours and neoplasia | ECE2013
Leroy Clara
, DoCao Christine
, Karrouz Wassila
, Le Guillou Anne-Claire
, Derveaux Alexandra
, Buisine Marie-Pierre
, Perbet R
, Leteurtre Emmanuelle
, Caiazzo Robert
, Pattou Francois
, Vantyghem Marie-Christine
Aggressive adreno-cortical carcinoma (ACC) is a rare, aggressive malignancy, with poorly understood molecular pathogenesis. As a result, therapeutic options are currently limited, surgery being currently the lone curative modality. Most cases of ACC are sporadic, although some familial cancer syndromes (LiFraumeni, BeckwithWiedemann, MEN1, Carney complex, congenital adrenal hyperplasia, etc.) are associated with an increased incidence of ACC. The genes involved in ...