ea0081p340 | Diabetes, Obesity, Metabolism and Nutrition | ECE2022
Cecchetti Carolina
, Belardinelli Elisabetta
, Dionese Paola
, Teglia Rita
, Di Cintio Ilaria
, D'apice Maria Rosaria
, Pagotto Uberto
, Gambineri Alessandra
Background and Objective: Severe metabolic complications generally manifest at an early age in Berardinelli Seip congenital lipodystrophy (BSCL) and their management is especially challenging, often requiring prompt pharmacological treatment with insulin-sensitizers, lipid lowering drugs, insulin and eventually metreleptin. Nutritional intervention with low lipid personalized diets is considered by experts a fundamental tool in handling the disease when associated with ...