ea0090p121 | Endocrine-related Cancer | ECE2023
Krausova Adela
, Limanova Zdenka
, Sedlačkova Eva
, Schutzner Jan
, Michalsky David
, Hana Vaclav
, Jiskra Jan
Introduction: Cushings syndrome (CS) is a rare disease with incidence estimated 2-4 cases per million inhabitants per year. ACTH-dependent forms comprise up to 80% of all cases, of which 80% are central and 20% are ectopic, paraneoplastic forms of ACTH-dependent CS. Thymic neuroendocrine tumors (NET) are accounting for 0,4 - 3% of all NETs with incidence of 0.02/100 000 inhabitants/year. Up to one third of them are hormonally active (secrete adrenocorticotropic hor...