ea0063gp187 | Adrenal and Neuroendocrine - Clinical | ECE2019
Improda Nicola
, Esposito Andrea
, Capalbo Donatella
, Cappa Marco
, Ferro Giusy
, Balsamo Antonio
, Baronio Federico
, Russo Gianni
, Lascio Alessandra Di
, Greggio Nella Augusta
, Tosetto Ilaria
, Valenzise Mariella
, Wasniewska Malgorzata
, Maghnie Mohamad
, Radetti Giorgio
, Longhi Silvia
, Betterle Corrado
, Salerno Mariacarolina
Background: Primary Adrenal Insufficiency (PAI) is a rare life-threatening disorder. Data on etiology and outcome of PAI in childhood are scanty, with the exception of Congenital Adrenal Hyperplasia (CAH) due to 21-hydroxylase deficiency (21OHD). The aim of our study is to evaluate etiology, morbidity and long-term outcome of PAI in a large cohort of children and characterize clinical presentation in subjects with PAI not due to 21OHD CAH.Material and me...