: In this paper we present an 18-year-old patient with Klinefelter syndrome who has taurodontism. Klinefelter syndrome is the most common abnormality of sex chromosomes. It is characterized by hypogonadism, gynaecomastia, azoospermia or oligospermia, and increased levels of gonadotropins. Associated medical disorders can be categorized as follows; cancer, autoimmune disorders, intellectuel and psychiatric disorder, osteoporosis, endocrine disorders, venous disease and taurodontism. Taurodontism is a developmental anomaly of a tooth characterized by large pulp chamber and short roots. It affects 0.53% of the general population. Taurodontism is observed with several syndromes and anomalies including Klinefelter syndrome. Endodontic treatment of taurodont teeth is tend to be complex and difficult because of the complexity in the tooth morphology, extraction of the taurodont teeth may be difficult and these teeth have risk for early decay. This feature can be seen in permanent and primary teeth, in a single tooth, or in several molars, and can be unilateral or bilateral. Taurodontism must be the part of comorbidity evaluation and patients with Klinefelter syndrome should have regular dental examination and care in order to provide long term oral health and improve quality of life of patients with Klinefelter syndrome.
20 May 2017 - 23 May 2017